A giant retroperitoneal lymphangioma in a patient with neurofibromatosis type 1

• Published in: Annals of surgical treatment and research pp. 43 - 46
• Main Authors: Jeong Ho Kim, 김민옥, Young Jin Choi, 한현영, 박강서, 조병선, 강동욱
• Format: Journal Article
• Language: English
• Published: 대한외과학회 01.06.2011
• Subjects: 일반외과학
• ISSN: 2288-6575; 2288-6796

Neurofibromatosis type 1 (NF-1) is a genetically inherited disorder that may cause skin abnormalities and tumors that form on nerve tissues. These tumors can be small or large and can occur anywhere in the body, including the brain, spinal cord, or other peripheral nerves. Retroperitoneal lymphangiomas are very rare benign malformations of the lymphatic system. About 95% lymphangiomas occur in the skin and the subcutaneous tissues of the head, neck and axillary region and the remaining 5% appear in other parts of the body such as lungs, pleura, pericardium, liver, gallbladder, kidney, and the mesentery. Herein, we report the case of a giant retroperitoneal lymphangioma in a patient with NF-1 with a review of the literature. KCI Citation Count: 3