舌咽,迷走神経障害をともなったChurg-Strauss症候群の1例
Churg-Strauss症候群(CSS)の経過中に頭痛と舌咽・迷走神経障害を呈した60歳の男性例を経験した.患者はCSSにともなう多発単神経障害で入院し,ステロイドパルス療法後にプレドニゾロン(PSL)内服をおこない改善した.退院3カ月後,頭痛と嚥下障害・嗄声が出現し,舌咽・迷走神経障害をみとめた.CSSにともなう脳神経障害と判断し,ステロイドパルス療法を追加したところ頭痛と嚥下障害は改善した.2カ月後,PSL漸減中に頭痛の再燃と左顔面のしびれ感が出現したが,PSL増量により軽快した.CSSで脳神経障害を呈することは比較的少なく,とくに舌咽・迷走神経といった下位脳神経障害の報告は過去に1例の...
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| Published in | 臨床神経学 Vol. 52; no. 7; pp. 507 - 510 |
|---|---|
| Main Authors | , , , , , |
| Format | Journal Article |
| Language | Japanese |
| Published |
日本神経学会
2012
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| Subjects | |
| Online Access | Get full text |
| ISSN | 0009-918X 1882-0654 |
| DOI | 10.5692/clinicalneurol.52.507 |
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| Abstract | Churg-Strauss症候群(CSS)の経過中に頭痛と舌咽・迷走神経障害を呈した60歳の男性例を経験した.患者はCSSにともなう多発単神経障害で入院し,ステロイドパルス療法後にプレドニゾロン(PSL)内服をおこない改善した.退院3カ月後,頭痛と嚥下障害・嗄声が出現し,舌咽・迷走神経障害をみとめた.CSSにともなう脳神経障害と判断し,ステロイドパルス療法を追加したところ頭痛と嚥下障害は改善した.2カ月後,PSL漸減中に頭痛の再燃と左顔面のしびれ感が出現したが,PSL増量により軽快した.CSSで脳神経障害を呈することは比較的少なく,とくに舌咽・迷走神経といった下位脳神経障害の報告は過去に1例のみと稀少なため報告する. |
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| AbstractList | Churg-Strauss症候群(CSS)の経過中に頭痛と舌咽・迷走神経障害を呈した60歳の男性例を経験した.患者はCSSにともなう多発単神経障害で入院し,ステロイドパルス療法後にプレドニゾロン(PSL)内服をおこない改善した.退院3カ月後,頭痛と嚥下障害・嗄声が出現し,舌咽・迷走神経障害をみとめた.CSSにともなう脳神経障害と判断し,ステロイドパルス療法を追加したところ頭痛と嚥下障害は改善した.2カ月後,PSL漸減中に頭痛の再燃と左顔面のしびれ感が出現したが,PSL増量により軽快した.CSSで脳神経障害を呈することは比較的少なく,とくに舌咽・迷走神経といった下位脳神経障害の報告は過去に1例のみと稀少なため報告する. |
| Author | 冨本, 秀和 上田, 有紀人 島田, 拓弥 伊井, 裕一郎 谷口, 彰 佐々木, 良元 |
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| References | 3) Della Rossa A, Baldini C, Tavoni A, et al. Churg-Strauss syndrome: clinical and serological features of 19 patients from a single Italian centre. Rheumatology 2002;41:1286-1294. 8) Morinaga A, Ono K, Komai K, et al. Microscopic polyangitis presenting with temporal arteritis and multiple cranial neuropathies. J Neurol Sci 2007;256:81-83. 1) Guillevin L, Cohen P, Gayraud M, et al. Churg-Strauss syndrome. Clinical study and long-term follow-up of 96 patients. Medicine 1999;78:26-37. 4) Sinico RA, Di Toma L, Maggiore U, et al. Prevalence and clinical significance of antineutrophil cytoplasmic antibodies in Churg-Strauss syndrome. Arthritis Rheum 2005;52:2926-2935. 9) Tokumaru AM, Obata T, Kohyama S, et al. Intracranial meningeal involvement in Churg-Strauss syndrome. AJNR Am J Neuroradiol 2002;23:221-224. 10) Jacobi D, Maillot F, Hommet C, et al. P-ANCA cranial pachymeningitis: a case report. Clin Rheumatol 2005;24:174-177. 5) Sablé-Fourtassou R, Cohen P, Mahr A, et al. Antineutrophil cytoplasmic antibodies and the Churg-Strauss syndrome. Ann Intern Med 2005;143:632-638. 2) Solans R, Bosch JA, Pérez-Bocanegra C, et al. Churg-Strauss syndrome: outcome and long-term follow-up of 32 patients. Rheumatology 2001;40:763-771. 6) Wolf J, Bergner R, Mutallib S, et al. Neurologic complications of Churg-Strauss syndrome -a prospective monocentric study. Eur J Neurol 2010;17:582-588. 7) Mazzantini M, Fattori B, Matteucci F, et al. Neuro-laryngeal involvement in Churg-Strauss syndrome. Eur Arch Otorhinolaryngol 1998;255:302-306. |
| References_xml | – reference: 4) Sinico RA, Di Toma L, Maggiore U, et al. Prevalence and clinical significance of antineutrophil cytoplasmic antibodies in Churg-Strauss syndrome. Arthritis Rheum 2005;52:2926-2935. – reference: 9) Tokumaru AM, Obata T, Kohyama S, et al. Intracranial meningeal involvement in Churg-Strauss syndrome. AJNR Am J Neuroradiol 2002;23:221-224. – reference: 10) Jacobi D, Maillot F, Hommet C, et al. P-ANCA cranial pachymeningitis: a case report. Clin Rheumatol 2005;24:174-177. – reference: 7) Mazzantini M, Fattori B, Matteucci F, et al. Neuro-laryngeal involvement in Churg-Strauss syndrome. Eur Arch Otorhinolaryngol 1998;255:302-306. – reference: 2) Solans R, Bosch JA, Pérez-Bocanegra C, et al. Churg-Strauss syndrome: outcome and long-term follow-up of 32 patients. Rheumatology 2001;40:763-771. – reference: 3) Della Rossa A, Baldini C, Tavoni A, et al. Churg-Strauss syndrome: clinical and serological features of 19 patients from a single Italian centre. Rheumatology 2002;41:1286-1294. – reference: 8) Morinaga A, Ono K, Komai K, et al. Microscopic polyangitis presenting with temporal arteritis and multiple cranial neuropathies. J Neurol Sci 2007;256:81-83. – reference: 5) Sablé-Fourtassou R, Cohen P, Mahr A, et al. Antineutrophil cytoplasmic antibodies and the Churg-Strauss syndrome. Ann Intern Med 2005;143:632-638. – reference: 6) Wolf J, Bergner R, Mutallib S, et al. Neurologic complications of Churg-Strauss syndrome -a prospective monocentric study. Eur J Neurol 2010;17:582-588. – reference: 1) Guillevin L, Cohen P, Gayraud M, et al. Churg-Strauss syndrome. Clinical study and long-term follow-up of 96 patients. Medicine 1999;78:26-37. |
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| Snippet | Churg-Strauss症候群(CSS)の経過中に頭痛と舌咽・迷走神経障害を呈した60歳の男性例を経験した.患者はCSSにともなう多発単神経障害で入院し,ステロイドパルス療法... |
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| SubjectTerms | Churg-Strauss症候群 嚥下障害 舌咽神経障害 迷走神経障害 頭痛 |
| Title | 舌咽,迷走神経障害をともなったChurg-Strauss症候群の1例 |
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