Pedunculated Nodules as a Variant of Dermatofibrosarcoma Protuberans

• Published in: Annals of dermatology Vol. 28; no. 5; pp. 629 - 631
• Main Authors: Kim, Min Jung, Hur, Min Seok, Choi, Byung Gon, Kim, Soo Young, Lee, Yang Won, Choe, Yong Beom, Ahn, Kyu Joong
• Format: Journal Article
• Language: English
• Published: Korea (South) Korean Dermatological Association; The Korean Society for Investigative Dermatology 01.10.2016; 대한피부과학회
• Subjects: Case Report; 피부과학; Dermatofibrosarcoma protuberans; Multiple pedunculated nodules
• ISSN: 1013-9087; 2005-3894
• DOI: 10.5021/ad.2016.28.5.629

Dermatofibrosarcoma protuberans (DFSP) is a rare disease of dermal fibroblastic origin that accounts for less than 5% of all soft tissue sarcomas in adults. DFSP grows slowly and is an asymptomatic lesion at the initial diagnosis. Herein, we report a case of multiple pedunculated nodules as a variant of DFSP. A 47-year-old man presented with a 7-month history of multiple well-circumscribed, firm, pedunculated nodules on the inguinal area. Histopathologic examination results showed densely packed uniform spindle cells with a storiform and cartwheel pattern, and positivity for CD34. Wide excision and skin graft were performed and at the 6-month follow-up, there was no evidence of recurrence or metastasis.