A Case of Incontinentia Pigmenti Associated with Multiorgan Abnormalities

Incontinentia pigmenti is a systemic disorder affecting the skin, teeth, eyes, nervous tissue, hair, nails, musculoskeletal system, and heart. We describe an 11-month-old girl with incontinentia pigmenti associated with a ventricular septal defect, left hemiatrophy, hemangiomas, an abnormal labial f...

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Published inAnnals of dermatology Vol. 21; no. 1; pp. 56 - 59
Main Authors Chung, Woon-Kyong, Lee, Deok-Woo, Chang, Sung-Eun, Lee, Mi-Woo, Choi, Jee-Ho, Moon, Kee-Chan
Format Journal Article
LanguageEnglish
Published Korea (South) Korean Dermatological Association; The Korean Society for Investigative Dermatology 01.02.2009
대한피부과학회
Subjects
Case Report
피부과학
Genodermatosis
Systemic disorder
Incontinentia pigmenti
Online AccessGet full text
ISSN1013-9087
2005-3894
2005-3894
DOI10.5021/ad.2009.21.1.56

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Summary:Incontinentia pigmenti is a systemic disorder affecting the skin, teeth, eyes, nervous tissue, hair, nails, musculoskeletal system, and heart. We describe an 11-month-old girl with incontinentia pigmenti associated with a ventricular septal defect, left hemiatrophy, hemangiomas, an abnormal labial frenum, and spastic cerebral palsy manifested as left hemiplegia and developmental delay. We believe this patient illustrates that incontinentia pigmenti is a systemic disorder necessitating a multidisciplinary approach to management.
Bibliography:ObjectType-Case Study-2
SourceType-Scholarly Journals-1
ObjectType-Feature-4
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ObjectType-Report-1
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G704-002233.2009.21.1.025
ISSN:1013-9087
2005-3894
2005-3894
DOI:10.5021/ad.2009.21.1.56