名古屋大学における副腎皮質癌の診療の実際-内分泌外科の立場から
副腎皮質癌は予後不良な悪性腫瘍であり,難解な手術手技に加えて転移再発症例やcStage Ⅳ症例に対する集学的治療,ミトタン投与のマネージメントなど多岐にわたる診療が必要とされ,内分泌外科医の果たす役割は大きい。当科において,2004年から2020年の間に外科的切除を施行した副腎皮質癌は13例であり,年齢中央値68歳,男性3例で女性10例,右7例で左6例であった。開放手術10例(開胸開腹9例,開腹1例)で,腹腔鏡手術3例であった。病期分類はStage Ⅰが3例,Ⅱが3例,Ⅲが5例,Ⅳが1例であり,術後補助療法として7例にミトタンを投与した。7例に転移再発を認め,5例が無再発経過中である。副腎皮質...
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Published in | 日本内分泌・甲状腺外科学会雑誌 Vol. 37; no. 4; pp. 270 - 275 |
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Main Authors | , , , , , , , |
Format | Journal Article |
Language | Japanese |
Published |
日本内分泌外科学会・日本甲状腺外科学会
2020
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Subjects | |
Online Access | Get full text |
ISSN | 2186-9545 |
DOI | 10.11226/jaesjsts.37.4_270 |
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Abstract | 副腎皮質癌は予後不良な悪性腫瘍であり,難解な手術手技に加えて転移再発症例やcStage Ⅳ症例に対する集学的治療,ミトタン投与のマネージメントなど多岐にわたる診療が必要とされ,内分泌外科医の果たす役割は大きい。当科において,2004年から2020年の間に外科的切除を施行した副腎皮質癌は13例であり,年齢中央値68歳,男性3例で女性10例,右7例で左6例であった。開放手術10例(開胸開腹9例,開腹1例)で,腹腔鏡手術3例であった。病期分類はStage Ⅰが3例,Ⅱが3例,Ⅲが5例,Ⅳが1例であり,術後補助療法として7例にミトタンを投与した。7例に転移再発を認め,5例が無再発経過中である。副腎皮質癌は予後不良の疾患であり,完全切除を目指した手術手技や,集学的治療に対する幅広い知識を習得することが肝要である。 |
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AbstractList | 副腎皮質癌は予後不良な悪性腫瘍であり,難解な手術手技に加えて転移再発症例やcStage Ⅳ症例に対する集学的治療,ミトタン投与のマネージメントなど多岐にわたる診療が必要とされ,内分泌外科医の果たす役割は大きい。当科において,2004年から2020年の間に外科的切除を施行した副腎皮質癌は13例であり,年齢中央値68歳,男性3例で女性10例,右7例で左6例であった。開放手術10例(開胸開腹9例,開腹1例)で,腹腔鏡手術3例であった。病期分類はStage Ⅰが3例,Ⅱが3例,Ⅲが5例,Ⅳが1例であり,術後補助療法として7例にミトタンを投与した。7例に転移再発を認め,5例が無再発経過中である。副腎皮質癌は予後不良の疾患であり,完全切除を目指した手術手技や,集学的治療に対する幅広い知識を習得することが肝要である。 |
Author | 角田, 伸行 一川, 貴洋 添田, 郁美 柴田, 雅央 高野, 悠子 稲石, 貴弘 武内, 大 菊森, 豊根 |
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References | 6. Fassnacht M, Johanssen S, Quinkler M, et al.: Limited prognostic value of the 2004 International Union Against Cancer staging classification for adrenocortical carcinoma: proposal for a Revised TNM Classification. Cancer 115: 243-250, 2009 8. 菊森豊根,今井常夫:他臓器浸潤を伴う副腎腫瘍.日内分泌・甲状腺外会誌 29:113-117,2012 18. Jasim S, Habra MA: Management of Adrenocortical Carcinoma. Curr Oncol Rep 21: 20, 2019 20. Wang S, Gao WC, Chen SS, et al.: Primary site surgery for metastatic adrenocortical carcinoma improves survival outcomes: an analysis of a population-based database. Onco Targets Ther 10: 5311-5315, 2017 15. Simon G, Pattou F, Mirallié E, et al.: Surgery for recurrent adrenocortical carcinoma: A multicenter retrospective study. Surgery 161: 249-256, 2017 4. Miller BS, Gauger PG, Hammer GD, et al.: Proposal for modification of the ENSAT staging system for adrenocortical carcinoma using tumor grade. Langenbecks Arch Surg 395: 955-961, 2010 12. Autorino R, Bove P, De Sio M, et al.: Open Versus Laparoscopic Adrenalectomy for Adrenocortical Carcinoma: A Meta-analysis of Surgical and Oncological Outcomes. Ann Surg Oncol 23: 1195-1202, 2016 1. Kebebew E, Reiff E, Duh QY, et al.: Extent of disease at presentation and outcome for adrenocortical carcinoma: have we made progress? World J Surg 30: 872-878, 2006 14. Puglisi S, Perotti P, Barbot M, et al.: Preoperative treatment with Metyrapone in patients with Cushing's syndrome due to adrenal adenoma. Endocr Connect 7: 1227- , 2018 10. 山崎有人,中村保宏,佐藤文俊他:副腎皮質癌のマネージメントおよび治療標的因子について.日内分泌・甲状腺外会誌 32:239-242,2015 16. Berruti A, Baudin E, Gelderblom H, et al.: Adrenal cancer: ESMO Clinical Practice Guidelines for diagnosis, treatment and follow-up. Ann Oncol 23: 131-138, 2012 21. Calabrese A, Basile V, Puglisi S, et al.: Adjuvant mitotane therapy is beneficial in non-metastatic adrenocortical carcinoma at high risk of recurrence. Eur J Endocrinol 180: 387-396, 2019 9. 柴田雅央,稲石貴弘,宮嶋則行他:副腎皮質癌.日内分泌・甲状腺外会誌 33:36-40,2016 2. Kerkhofs TM, Verhoeven RH, Van der Zwan JM, et al.: Adrenocortical carcinoma: a population-based study on incidence and survival in the Netherlands since 199. Eur J Cancer 49: 2579-2586, 2013 7. Fassnacht M, Dekkers O, Else T, et al.: European Society of Endocrinology Clinical Practice Guidelines on the management of adrenocortical carcinoma in adults, in collaboration with the European Network for the Study of Adrenal Tumors. Eur J Endocrinol 179: 1-46, 2018 22. 内山将伸,原 周司,緒方憲太郎他:HPLCによる簡便なミトタン血中濃度測定法の開発および適用.医療薬学 38:191-195,2012 5. Datta J, Roses RE: Surgical Management of Adrenocortical Carcinoma: An Evidence-Based Approach. Surg Oncol Clin N Am 25: 153-170, 2016 17. Fassnacht M, Terzolo M, Allolio B, et al.: Combination chemotherapy in advanced adrenocortical carcinoma. N Engl J Med 366: 2189-2197, 2012 13. Donatini G, Caiazzo R, Do Cao C, et al.: Long-term survival after adrenalectomy for stage I/II adrenocortical carcinoma (ACC): a retrospective comparative cohort study of laparoscopic versus open approach. Ann Surg Oncol 21: 284-291, 2014 3. Allolio B, Fassnacht M: Clinical review: Adrenocortical carcinoma: clinical update. J Clin Endocrinol Metab 91: 2027-2037, 2006 11. Kerkhofs TM, Ettaieb MH, Hermsen IG, et al.: Developing treatment for adrenocortical carcinoma. Endocr Relat Cancer 22: 325-338, 2015 19. Bednarski BK, Habra MA, Phan A, et al.: Borderline resectable adrenal cortical carcinoma: a potential role for preoperative chemotherapy. World J Surg 38: 1318-1327, 2014 |
References_xml | – reference: 5. Datta J, Roses RE: Surgical Management of Adrenocortical Carcinoma: An Evidence-Based Approach. Surg Oncol Clin N Am 25: 153-170, 2016 – reference: 8. 菊森豊根,今井常夫:他臓器浸潤を伴う副腎腫瘍.日内分泌・甲状腺外会誌 29:113-117,2012 – reference: 4. Miller BS, Gauger PG, Hammer GD, et al.: Proposal for modification of the ENSAT staging system for adrenocortical carcinoma using tumor grade. Langenbecks Arch Surg 395: 955-961, 2010 – reference: 15. Simon G, Pattou F, Mirallié E, et al.: Surgery for recurrent adrenocortical carcinoma: A multicenter retrospective study. Surgery 161: 249-256, 2017 – reference: 1. Kebebew E, Reiff E, Duh QY, et al.: Extent of disease at presentation and outcome for adrenocortical carcinoma: have we made progress? World J Surg 30: 872-878, 2006 – reference: 14. Puglisi S, Perotti P, Barbot M, et al.: Preoperative treatment with Metyrapone in patients with Cushing's syndrome due to adrenal adenoma. Endocr Connect 7: 1227- , 2018 – reference: 6. Fassnacht M, Johanssen S, Quinkler M, et al.: Limited prognostic value of the 2004 International Union Against Cancer staging classification for adrenocortical carcinoma: proposal for a Revised TNM Classification. Cancer 115: 243-250, 2009 – reference: 11. Kerkhofs TM, Ettaieb MH, Hermsen IG, et al.: Developing treatment for adrenocortical carcinoma. Endocr Relat Cancer 22: 325-338, 2015 – reference: 7. Fassnacht M, Dekkers O, Else T, et al.: European Society of Endocrinology Clinical Practice Guidelines on the management of adrenocortical carcinoma in adults, in collaboration with the European Network for the Study of Adrenal Tumors. Eur J Endocrinol 179: 1-46, 2018 – reference: 10. 山崎有人,中村保宏,佐藤文俊他:副腎皮質癌のマネージメントおよび治療標的因子について.日内分泌・甲状腺外会誌 32:239-242,2015 – reference: 13. Donatini G, Caiazzo R, Do Cao C, et al.: Long-term survival after adrenalectomy for stage I/II adrenocortical carcinoma (ACC): a retrospective comparative cohort study of laparoscopic versus open approach. Ann Surg Oncol 21: 284-291, 2014 – reference: 17. Fassnacht M, Terzolo M, Allolio B, et al.: Combination chemotherapy in advanced adrenocortical carcinoma. N Engl J Med 366: 2189-2197, 2012 – reference: 22. 内山将伸,原 周司,緒方憲太郎他:HPLCによる簡便なミトタン血中濃度測定法の開発および適用.医療薬学 38:191-195,2012 – reference: 2. Kerkhofs TM, Verhoeven RH, Van der Zwan JM, et al.: Adrenocortical carcinoma: a population-based study on incidence and survival in the Netherlands since 199. Eur J Cancer 49: 2579-2586, 2013 – reference: 18. Jasim S, Habra MA: Management of Adrenocortical Carcinoma. Curr Oncol Rep 21: 20, 2019 – reference: 16. Berruti A, Baudin E, Gelderblom H, et al.: Adrenal cancer: ESMO Clinical Practice Guidelines for diagnosis, treatment and follow-up. Ann Oncol 23: 131-138, 2012 – reference: 21. Calabrese A, Basile V, Puglisi S, et al.: Adjuvant mitotane therapy is beneficial in non-metastatic adrenocortical carcinoma at high risk of recurrence. Eur J Endocrinol 180: 387-396, 2019 – reference: 9. 柴田雅央,稲石貴弘,宮嶋則行他:副腎皮質癌.日内分泌・甲状腺外会誌 33:36-40,2016 – reference: 12. Autorino R, Bove P, De Sio M, et al.: Open Versus Laparoscopic Adrenalectomy for Adrenocortical Carcinoma: A Meta-analysis of Surgical and Oncological Outcomes. Ann Surg Oncol 23: 1195-1202, 2016 – reference: 20. Wang S, Gao WC, Chen SS, et al.: Primary site surgery for metastatic adrenocortical carcinoma improves survival outcomes: an analysis of a population-based database. Onco Targets Ther 10: 5311-5315, 2017 – reference: 3. Allolio B, Fassnacht M: Clinical review: Adrenocortical carcinoma: clinical update. J Clin Endocrinol Metab 91: 2027-2037, 2006 – reference: 19. Bednarski BK, Habra MA, Phan A, et al.: Borderline resectable adrenal cortical carcinoma: a potential role for preoperative chemotherapy. World J Surg 38: 1318-1327, 2014 |
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SubjectTerms | 内分泌外科 副腎皮質癌 外科的切除 術後補助療法 集学的治療 |
Title | 名古屋大学における副腎皮質癌の診療の実際-内分泌外科の立場から |
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