長期間にわたって骨塩量の変化を定量的に検討し得た成人特発性Fanconi症候群の1例

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Published in日本腎臓学会誌 Vol. 39; no. 2; pp. 178 - 182
Main Authors 小路, 哲生, 橋本, 真由子, 藤岡, 宏, 松尾, 裕英, 高橋, 則尋, 藤田, 陽子, 湯淺, 繁一, 内田, 光一, 清元, 秀泰
Format Journal Article
LanguageJapanese
Published 社団法人 日本腎臓学会 1997
Online AccessGet full text
ISSN0385-2385
1884-0728
DOI10.14842/jpnjnephrol1959.39.178

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Author 藤岡, 宏
清元, 秀泰
藤田, 陽子
橋本, 真由子
内田, 光一
湯淺, 繁一
高橋, 則尋
小路, 哲生
松尾, 裕英
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  fullname: 内田, 光一
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  fullname: 清元, 秀泰
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References 17. Wahner HW, Dunn WL, Riggs BL. Assessment of bone mineral. Part 2. J Nucl Med 1984 ; 25 :1141 -1153.
8. Kurtz I, Maher T, Hulter HN, Schambelan M, Sebastian A. Effect of dirt on plasma acid base composition in normal humans. Kidney Int 1983 ; 24 : 670-680.
10. Medias NE, Johns CA, Homer SM. Independence of the acute acid buffering response from endogenous parathyroid hormone. Am J Physiol 1982 ; 243 : F 141-F 149.
18. Wahner HW, Dunn WL, Brown ML, Morin RL, Riggs BL. Comparison of dualenergy X-ray absorptiometry and dual photon absorptiometry for bone mineral measurements of the lumber spine. Mayo Clin Proc 1988 ; 63 :1075-1084.
4. Chesney RW, Novello AC. Defects of renal tubular transport. In : Massry SG, Glassock RJ (ed), Textbook of Nephrology : Williams and Wilkins, Baltimore, 1989 ; 445-460.
5. Clarke BL, Wynne AG, Wilson DM, Fizpatrick LA. Osteomalacia associated with adult Fanconi's syndrome : clin-ical and diagnostic features. Clin Endocrinol 1995 ; 43 : 479-490.
7. 小椋陽介,相沢純雄,尾田芳隆.尿細管性骨疾患.日本臨牀1986;44:2499-2506.
14. 柿崎 寛,斎藤 皓,山本和英.成人型Fanconi症候群の治療経験―1α-(OH)-D,による治療―.骨代謝1980;13:81-85.
2. Mikman LA. Multiple spontaneous idiopathic symmetrical fractures. Am J Roentgenol 1934 ; 32 : 622-634.
11. Beck N, Webster SK. Effect of acute metabolic acidosis on parathyroid hormone action and calcium mobilization. Am J Physiol 1976 ; 230 :127-131.
1. Brewer ED. The Fanconi syndrome. In : Gonick HC, Buckalew VW Jr (ed), Renal Tubular Disorders : Marcel Dekker Inc, New York, 1985 : 475-544.
13. 吉川靖三,中村利孝,鴨川盛秀,大内美南.特発性Fanconi症候群4例の治療経験骨代謝1978;11:220-231.
15. 広瀬源二郎,小副川 寛.活性型ビタミンDにより寛解した成人型Fanconi症候群にみられた神経原性筋萎縮と骨軟化.臨床神経学1981;21;698-701.
3. Stower JM, Dent CE. Studies on the mechanisim of the Fanconi syndrome. QJ Med 1947 ; 16 : 275-290.
16. Wahner HW, Dunn WL, Riggs BL. Assessment of bone mineral. Part 1. J Nucl Med 1984; 25 :1134 -1141.
9. Weber HP, Gray RW, Dominguez JH, Lemann J Jr. The lack of effect of chronic metabolic acidosis on 25-OH-vitamin D metabolism and serum parathyroid hormone in human. J Clin Endocrinol Metab 1976 ; 43 : 1047-1055.
12. Cunningham J, Bikle DD, Avioli LV. Acute, but not chronic metabolic acidosis disturbs 25-hydroxyvitamin D3 metabolism. Kidney Int 1984 ; 25 : 47-52.
6. Wallis LA, Engle RL. The adult Fanconi Syndrome. II, Review of eighteen cases. Am J Med 1957 ; 22 :13 -23
References_xml – reference: 9. Weber HP, Gray RW, Dominguez JH, Lemann J Jr. The lack of effect of chronic metabolic acidosis on 25-OH-vitamin D metabolism and serum parathyroid hormone in human. J Clin Endocrinol Metab 1976 ; 43 : 1047-1055.
– reference: 18. Wahner HW, Dunn WL, Brown ML, Morin RL, Riggs BL. Comparison of dualenergy X-ray absorptiometry and dual photon absorptiometry for bone mineral measurements of the lumber spine. Mayo Clin Proc 1988 ; 63 :1075-1084.
– reference: 12. Cunningham J, Bikle DD, Avioli LV. Acute, but not chronic metabolic acidosis disturbs 25-hydroxyvitamin D3 metabolism. Kidney Int 1984 ; 25 : 47-52.
– reference: 5. Clarke BL, Wynne AG, Wilson DM, Fizpatrick LA. Osteomalacia associated with adult Fanconi's syndrome : clin-ical and diagnostic features. Clin Endocrinol 1995 ; 43 : 479-490.
– reference: 11. Beck N, Webster SK. Effect of acute metabolic acidosis on parathyroid hormone action and calcium mobilization. Am J Physiol 1976 ; 230 :127-131.
– reference: 16. Wahner HW, Dunn WL, Riggs BL. Assessment of bone mineral. Part 1. J Nucl Med 1984; 25 :1134 -1141.
– reference: 2. Mikman LA. Multiple spontaneous idiopathic symmetrical fractures. Am J Roentgenol 1934 ; 32 : 622-634.
– reference: 1. Brewer ED. The Fanconi syndrome. In : Gonick HC, Buckalew VW Jr (ed), Renal Tubular Disorders : Marcel Dekker Inc, New York, 1985 : 475-544.
– reference: 4. Chesney RW, Novello AC. Defects of renal tubular transport. In : Massry SG, Glassock RJ (ed), Textbook of Nephrology : Williams and Wilkins, Baltimore, 1989 ; 445-460.
– reference: 15. 広瀬源二郎,小副川 寛.活性型ビタミンDにより寛解した成人型Fanconi症候群にみられた神経原性筋萎縮と骨軟化.臨床神経学1981;21;698-701.
– reference: 17. Wahner HW, Dunn WL, Riggs BL. Assessment of bone mineral. Part 2. J Nucl Med 1984 ; 25 :1141 -1153.
– reference: 6. Wallis LA, Engle RL. The adult Fanconi Syndrome. II, Review of eighteen cases. Am J Med 1957 ; 22 :13 -23
– reference: 7. 小椋陽介,相沢純雄,尾田芳隆.尿細管性骨疾患.日本臨牀1986;44:2499-2506.
– reference: 8. Kurtz I, Maher T, Hulter HN, Schambelan M, Sebastian A. Effect of dirt on plasma acid base composition in normal humans. Kidney Int 1983 ; 24 : 670-680.
– reference: 14. 柿崎 寛,斎藤 皓,山本和英.成人型Fanconi症候群の治療経験―1α-(OH)-D,による治療―.骨代謝1980;13:81-85.
– reference: 10. Medias NE, Johns CA, Homer SM. Independence of the acute acid buffering response from endogenous parathyroid hormone. Am J Physiol 1982 ; 243 : F 141-F 149.
– reference: 13. 吉川靖三,中村利孝,鴨川盛秀,大内美南.特発性Fanconi症候群4例の治療経験骨代謝1978;11:220-231.
– reference: 3. Stower JM, Dent CE. Studies on the mechanisim of the Fanconi syndrome. QJ Med 1947 ; 16 : 275-290.
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Title 長期間にわたって骨塩量の変化を定量的に検討し得た成人特発性Fanconi症候群の1例
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