初回治療から10年後に再発したリンパ形質細胞リンパ腫・ワルデンシュトレームマクログロブリン血症に対してチラブルチニブが奏効した高齢患者の一例

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Published in天理医学紀要 Vol. 28; no. 1; pp. 54 - 58
Main Authors 中西 司, 丸山 亙, 大野 仁嗣, 竹岡 加陽, 羽白 高, 橋本 成修, 大谷 旭, 前川 ふみよ, 住吉 真治
Format Journal Article
LanguageEnglish
Published 公益財団法人 天理よろづ相談所 医学研究所 2025
Subjects
Online AccessGet full text
ISSN1344-1817
2187-2244
DOI10.12936/tenrikiyo.28-006

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Author 橋本 成修
羽白 高
中西 司
大野 仁嗣
大谷 旭
前川 ふみよ
竹岡 加陽
丸山 亙
住吉 真治
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References 4) Nakayama Y, Iioka F, Toda Y, et al. Lymphoplasmacytic lymphoma with the MYD88L265P mutation, producing non-IgM monoclonal immunoglobulins: 4 case reports. Tenri Med Bull 2019;22:12-28.
8) Montes-Moreno S, Geddie WR, Kersten MJ, et al. Lymphoplasmacytic lymphoma. The WHO Classification of Tumours Editorial Board. Haematolymphoid Tumours. 5th ed. Lyon: International Agency for Research on Cancer; 2025:394-398.
3) van Dongen JJ, Langerak AW, Brüggemann M, et al. Design and standardization of PCR primers and protocols for detection of clonal immunoglobulin and T-cell receptor gene recombinations in suspect lymphoproliferations: report of the BIOMED-2 Concerted Action BMH4-CT98-3936. Leukemia 2003;17:2257-2317.
6) Sekiguchi N, Rai S, Munakata W, et al. A multicenter, open-label, phase II study of tirabrutinib (ONO/GS-4059) in patients with Waldenström's macroglobulinemia. Cancer Sci 2020;111:3327-3337.
9) Freedman A. Clinical manifestations, pathologic features, and diagnosis of lymphoplasmacytic lymphoma. In: Lister A, ed. UpToDate (accessed on January 24, 2025); 2025.
2) Tedeschi A, Benevolo G, Varettoni M, et al. Fludarabine plus cyclophosphamide and rituximab in Waldenstrom macroglobulinemia: an effective but myelosuppressive regimen to be offered to patients with advanced disease. Cancer 2012;118:434-443.
1) Ansell SM. Epidemiology, pathogenesis, clinical manifestations, and diagnosis of Waldenström macroglobulinemia. In: Rajkumar SV, ed. UpToDate (accessed on January 24, 2025); 2025.
7) Sekiguchi N, Rai S, Munakata W, et al. Two-year outcomes of tirabrutinib monotherapy in Waldenström's macroglobulinemia. Cancer Sci 2022;113:2085-2096.
5) Ansell SM. Treatment and prognosis of Waldenström macroglobulinemia. In: Rajkumar SV, ed. UpToDate (accessed on January 24, 2025); 2025.
References_xml – reference: 1) Ansell SM. Epidemiology, pathogenesis, clinical manifestations, and diagnosis of Waldenström macroglobulinemia. In: Rajkumar SV, ed. UpToDate (accessed on January 24, 2025); 2025.
– reference: 3) van Dongen JJ, Langerak AW, Brüggemann M, et al. Design and standardization of PCR primers and protocols for detection of clonal immunoglobulin and T-cell receptor gene recombinations in suspect lymphoproliferations: report of the BIOMED-2 Concerted Action BMH4-CT98-3936. Leukemia 2003;17:2257-2317.
– reference: 6) Sekiguchi N, Rai S, Munakata W, et al. A multicenter, open-label, phase II study of tirabrutinib (ONO/GS-4059) in patients with Waldenström's macroglobulinemia. Cancer Sci 2020;111:3327-3337.
– reference: 5) Ansell SM. Treatment and prognosis of Waldenström macroglobulinemia. In: Rajkumar SV, ed. UpToDate (accessed on January 24, 2025); 2025.
– reference: 4) Nakayama Y, Iioka F, Toda Y, et al. Lymphoplasmacytic lymphoma with the MYD88L265P mutation, producing non-IgM monoclonal immunoglobulins: 4 case reports. Tenri Med Bull 2019;22:12-28.
– reference: 8) Montes-Moreno S, Geddie WR, Kersten MJ, et al. Lymphoplasmacytic lymphoma. The WHO Classification of Tumours Editorial Board. Haematolymphoid Tumours. 5th ed. Lyon: International Agency for Research on Cancer; 2025:394-398.
– reference: 7) Sekiguchi N, Rai S, Munakata W, et al. Two-year outcomes of tirabrutinib monotherapy in Waldenström's macroglobulinemia. Cancer Sci 2022;113:2085-2096.
– reference: 9) Freedman A. Clinical manifestations, pathologic features, and diagnosis of lymphoplasmacytic lymphoma. In: Lister A, ed. UpToDate (accessed on January 24, 2025); 2025.
– reference: 2) Tedeschi A, Benevolo G, Varettoni M, et al. Fludarabine plus cyclophosphamide and rituximab in Waldenstrom macroglobulinemia: an effective but myelosuppressive regimen to be offered to patients with advanced disease. Cancer 2012;118:434-443.
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SubjectTerms MYD88 p.L265P変異
チラブルチニブ
リンパ形質細胞リンパ腫・ワルデンシュトレームマクログロブリン血症
超音波気管支鏡ガイド下針生検
Title 初回治療から10年後に再発したリンパ形質細胞リンパ腫・ワルデンシュトレームマクログロブリン血症に対してチラブルチニブが奏効した高齢患者の一例
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Volume 28
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