Estimates of penetrance for recurrent pathogenic copy-number variations

Although an increasing number of copy-number variations are being identified as susceptibility loci for a variety of pediatric diseases, the penetrance of these copy-number variations remains mostly unknown. This poses challenges for counseling, both for recurrence risks and prenatal diagnosis. We s...

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Published inGenetics in medicine Vol. 15; no. 6; pp. 478 - 481
Main Authors Rosenfeld, Jill A., Coe, Bradley P., Eichler, Evan E., Cuckle, Howard, Shaffer, Lisa G.
Format Journal Article
LanguageEnglish
Published New York Elsevier Inc 01.06.2013
Nature Publishing Group US
Elsevier Limited
Nature Publishing Group
Subjects
Online AccessGet full text
ISSN1098-3600
1530-0366
1530-0366
DOI10.1038/gim.2012.164

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Abstract Although an increasing number of copy-number variations are being identified as susceptibility loci for a variety of pediatric diseases, the penetrance of these copy-number variations remains mostly unknown. This poses challenges for counseling, both for recurrence risks and prenatal diagnosis. We sought to provide empiric estimates for penetrance for some of these recurrent, disease-susceptibility loci. We conducted a Bayesian analysis, based on the copy-number variation frequencies in control populations (n = 22,246) and in our database of >48,000 postnatal microarray-based comparative genomic hybridization samples. The background risk for congenital anomalies/developmental delay/intellectual disability was assumed to be ~5%. Copy-number variations studied were 1q21.1 proximal duplications, 1q21.1 distal deletions and duplications, 15q11.2 deletions, 16p13.11 deletions, 16p12.1 deletions, 16p11.2 proximal and distal deletions and duplications, 17q12 deletions and duplications, and 22q11.21 duplications. Estimates for the risk of an abnormal phenotype ranged from 10.4% for 15q11.2 deletions to 62.4% for distal 16p11.2 deletions. This model can be used to provide more precise estimates for the chance of an abnormal phenotype for many copy-number variations encountered in the prenatal setting. By providing the penetrance, additional, critical information can be given to prospective parents in the genetic counseling session. Genet Med 2013:15(6):478–481
AbstractList Although an increasing number of copy-number variations are being identified as susceptibility loci for a variety of pediatric diseases, the penetrance of these copy-number variations remains mostly unknown. This poses challenges for counseling, both for recurrence risks and prenatal diagnosis. We sought to provide empiric estimates for penetrance for some of these recurrent, disease-susceptibility loci. We conducted a Bayesian analysis, based on the copy-number variation frequencies in control populations (n = 22,246) and in our database of >48,000 postnatal microarray-based comparative genomic hybridization samples. The background risk for congenital anomalies/developmental delay/intellectual disability was assumed to be ~5%. Copy-number variations studied were 1q21.1 proximal duplications, 1q21.1 distal deletions and duplications, 15q11.2 deletions, 16p13.11 deletions, 16p12.1 deletions, 16p11.2 proximal and distal deletions and duplications, 17q12 deletions and duplications, and 22q11.21 duplications. Estimates for the risk of an abnormal phenotype ranged from 10.4% for 15q11.2 deletions to 62.4% for distal 16p11.2 deletions. This model can be used to provide more precise estimates for the chance of an abnormal phenotype for many copy-number variations encountered in the prenatal setting. By providing the penetrance, additional, critical information can be given to prospective parents in the genetic counseling session.
Although an increasing number of copy-number variations are being identified as susceptibility loci for a variety of pediatric diseases, the penetrance of these copy-number variations remains mostly unknown. This poses challenges for counseling, both for recurrence risks and prenatal diagnosis. We sought to provide empiric estimates for penetrance for some of these recurrent, disease-susceptibility loci.PURPOSEAlthough an increasing number of copy-number variations are being identified as susceptibility loci for a variety of pediatric diseases, the penetrance of these copy-number variations remains mostly unknown. This poses challenges for counseling, both for recurrence risks and prenatal diagnosis. We sought to provide empiric estimates for penetrance for some of these recurrent, disease-susceptibility loci.We conducted a Bayesian analysis, based on the copy-number variation frequencies in control populations (n = 22,246) and in our database of >48,000 postnatal microarray-based comparative genomic hybridization samples. The background risk for congenital anomalies/developmental delay/intellectual disability was assumed to be ~5%. Copy-number variations studied were 1q21.1 proximal duplications, 1q21.1 distal deletions and duplications, 15q11.2 deletions, 16p13.11 deletions, 16p12.1 deletions, 16p11.2 proximal and distal deletions and duplications, 17q12 deletions and duplications, and 22q11.21 duplications.METHODSWe conducted a Bayesian analysis, based on the copy-number variation frequencies in control populations (n = 22,246) and in our database of >48,000 postnatal microarray-based comparative genomic hybridization samples. The background risk for congenital anomalies/developmental delay/intellectual disability was assumed to be ~5%. Copy-number variations studied were 1q21.1 proximal duplications, 1q21.1 distal deletions and duplications, 15q11.2 deletions, 16p13.11 deletions, 16p12.1 deletions, 16p11.2 proximal and distal deletions and duplications, 17q12 deletions and duplications, and 22q11.21 duplications.Estimates for the risk of an abnormal phenotype ranged from 10.4% for 15q11.2 deletions to 62.4% for distal 16p11.2 deletions.RESULTSEstimates for the risk of an abnormal phenotype ranged from 10.4% for 15q11.2 deletions to 62.4% for distal 16p11.2 deletions.This model can be used to provide more precise estimates for the chance of an abnormal phenotype for many copy-number variations encountered in the prenatal setting. By providing the penetrance, additional, critical information can be given to prospective parents in the genetic counseling session.CONCLUSIONThis model can be used to provide more precise estimates for the chance of an abnormal phenotype for many copy-number variations encountered in the prenatal setting. By providing the penetrance, additional, critical information can be given to prospective parents in the genetic counseling session.
Purpose:Although an increasing number of copy-number variations are being identified as susceptibility loci for a variety of pediatric diseases, the penetrance of these copy-number variations remains mostly unknown. This poses challenges for counseling, both for recurrence risks and prenatal diagnosis. We sought to provide empiric estimates for penetrance for some of these recurrent, disease-susceptibility loci.Methods:We conducted a Bayesian analysis, based on the copy-number variation frequencies in control populations (n = 22,246) and in our database of >48,000 postnatal microarray-based comparative genomic hybridization samples. The background risk for congenital anomalies/developmental delay/intellectual disability was assumed to be ~5%. Copy-number variations studied were 1q21.1 proximal duplications, 1q21.1 distal deletions and duplications, 15q11.2 deletions, 16p13.11 deletions, 16p12.1 deletions, 16p11.2 proximal and distal deletions and duplications, 17q12 deletions and duplications, and 22q11.21 duplications.Results:Estimates for the risk of an abnormal phenotype ranged from 10.4% for 15q11.2 deletions to 62.4% for distal 16p11.2 deletions.Conclusion:This model can be used to provide more precise estimates for the chance of an abnormal phenotype for many copy-number variations encountered in the prenatal setting. By providing the penetrance, additional, critical information can be given to prospective parents in the genetic counseling session.Genet Med 2013:15(6):478–481
Purpose: Although an increasing number of copy-number variations are being identified as susceptibility loci for a variety of pediatric diseases, the penetrance of these copy-number variations remains mostly unknown. This poses challenges for counseling, both for recurrence risks and prenatal diagnosis. We sought to provide empiric estimates for penetrance for some of these recurrent, disease-susceptibility loci. Methods: We conducted a Bayesian analysis, based on the copy-number variation frequencies in control populations ( n = 22,246) and in our database of >48,000 postnatal microarray-based comparative genomic hybridization samples. The background risk for congenital anomalies/developmental delay/intellectual disability was assumed to be ~5%. Copy-number variations studied were 1q21.1 proximal duplications, 1q21.1 distal deletions and duplications, 15q11.2 deletions, 16p13.11 deletions, 16p12.1 deletions, 16p11.2 proximal and distal deletions and duplications, 17q12 deletions and duplications, and 22q11.21 duplications. Results: Estimates for the risk of an abnormal phenotype ranged from 10.4% for 15q11.2 deletions to 62.4% for distal 16p11.2 deletions. Conclusion: This model can be used to provide more precise estimates for the chance of an abnormal phenotype for many copy-number variations encountered in the prenatal setting. By providing the penetrance, additional, critical information can be given to prospective parents in the genetic counseling session. Genet Med 2013:15(6):478–481
Although an increasing number of copy-number variations are being identified as susceptibility loci for a variety of pediatric diseases, the penetrance of these copy-number variations remains mostly unknown. This poses challenges for counseling, both for recurrence risks and prenatal diagnosis. We sought to provide empiric estimates for penetrance for some of these recurrent, disease-susceptibility loci. We conducted a Bayesian analysis, based on the copy-number variation frequencies in control populations (n = 22,246) and in our database of >48,000 postnatal microarray-based comparative genomic hybridization samples. The background risk for congenital anomalies/developmental delay/intellectual disability was assumed to be ~5%. Copy-number variations studied were 1q21.1 proximal duplications, 1q21.1 distal deletions and duplications, 15q11.2 deletions, 16p13.11 deletions, 16p12.1 deletions, 16p11.2 proximal and distal deletions and duplications, 17q12 deletions and duplications, and 22q11.21 duplications. Estimates for the risk of an abnormal phenotype ranged from 10.4% for 15q11.2 deletions to 62.4% for distal 16p11.2 deletions. This model can be used to provide more precise estimates for the chance of an abnormal phenotype for many copy-number variations encountered in the prenatal setting. By providing the penetrance, additional, critical information can be given to prospective parents in the genetic counseling session. Genet Med 2013:15(6):478–481
Purpose: Although an increasing number of copy-number variations are being identified as susceptibility loci for a variety of pediatric diseases, the penetrance of these copy-number variations remains mostly unknown. This poses challenges for counseling, both for recurrence risks and prenatal diagnosis. We sought to provide empiric estimates for penetrance for some of these recurrent, disease-susceptibility loci. Methods: We conducted a Bayesian analysis, based on the copy-number variation frequencies in control populations (n = 22,246) and in our database of >48,000 postnatal microarray-based comparative genomic hybridization samples. The background risk for congenital anomalies/developmental delay/intellectual disability was assumed to be approximately 5%. Copy-number variations studied were 1q21.1 proximal duplications, 1q21.1 distal deletions and duplications, 15q11.2 deletions, 16p13.11 deletions, 16p12.1 deletions, 16p11.2 proximal and distal deletions and duplications, 17q12 deletions and duplications, and 22q11.21 duplications. Results: Estimates for the risk of an abnormal phenotype ranged from 10.4% for 15q11.2 deletions to 62.4% for distal 16p11.2 deletions. Conclusion: This model can be used to provide more precise estimates for the chance of an abnormal phenotype for many copy-number variations encountered in the prenatal setting. By providing the penetrance, additional, critical information can be given to prospective parents in the genetic counseling session.
Author Cuckle, Howard
Eichler, Evan E.
Shaffer, Lisa G.
Coe, Bradley P.
Rosenfeld, Jill A.
Author_xml – sequence: 1
  givenname: Jill A.
  surname: Rosenfeld
  fullname: Rosenfeld, Jill A.
  organization: Signature Genomic Laboratories, PerkinElmer, Inc. Spokane, Washington, USA
– sequence: 2
  givenname: Bradley P.
  surname: Coe
  fullname: Coe, Bradley P.
  organization: Department of Genome Sciences, University of Washington, Seattle, Washington, USA
– sequence: 3
  givenname: Evan E.
  surname: Eichler
  fullname: Eichler, Evan E.
  organization: Department of Genome Sciences, University of Washington, Seattle, Washington, USA
– sequence: 4
  givenname: Howard
  surname: Cuckle
  fullname: Cuckle, Howard
  organization: Department of Obstetrics and Gynecology, Columbia University Medical Center, New York, New York, USA
– sequence: 5
  givenname: Lisa G.
  surname: Shaffer
  fullname: Shaffer, Lisa G.
  email: lshaffer@pawprintgenetics.com
  organization: Signature Genomic Laboratories, PerkinElmer, Inc. Spokane, Washington, USA
BackLink https://www.ncbi.nlm.nih.gov/pubmed/23258348$$D View this record in MEDLINE/PubMed
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Cites_doi 10.1056/NEJMoa0805384
10.1093/hmg/ddq259
10.1016/j.ajhg.2010.04.006
10.1542/peds.2009-1684
10.1146/annurev-genet-102209-163544
10.1136/jmg.2008.063412
10.1097/GIM.0b013e31822c79f9
10.1097/GIM.0b013e3182076c0c
10.1002/cem.1123
10.1002/pd.3945
10.1056/NEJMoa1200395
10.1038/ejhg.2010.102
10.1111/j.1471-0528.2012.03279.x
10.1038/ng.909
10.1111/j.1399-0004.2008.01094.x
10.1093/hmg/ddq366
10.1002/ajmg.a.30621
10.1186/1755-8166-1-8
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Issue 6
Keywords microarray
prenatal diagnosis
genomic disorder
copy-number variation
penetrance
Language English
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References Girirajan, Eichler (bb0010) 2010; 19
Shen, Dies, Holm (bb0040) 2010; 125
Baird, Anderson, Newcombe, Lowry (bb0080) 1988; 42
Walsh, Bracken (bb0090) 2011; 13
Miller, Adam, Aradhya (bb0035) 2010; 86
Girirajan, Rosenfeld, Coe (bb0045) 2012; 367
Ballif, Theisen, Coppinger (bb0050) 2008; 1
Lee, Lin, Lin, Shih, Lin, Su (bb0100) 2012; 119
Duker, Ballif, Bawle (bb0060) 2010; 18
Girirajan, Campbell, Eichler (bb0015) 2011; 45
van Bon, Mefford, Menten (bb0085) 2009; 46
Vassos, Collier, Holden (bb0075) 2010; 19
Mefford, Sharp, Baker (bb0020) 2008; 359
Cooper, Coe, Girirajan (bb0025) 2011; 43
Ballif, Theisen, McDonald-McGinn (bb0055) 2008; 74
Kaminsky, Kaul, Paschall (bb0030) 2011; 13
Shaffer, Dabell, Fisher (bb0105) 2012; 32
Hubert, Van der Veeken (bb0070) 2008; 22
Centers for Disease Control and Prevention (bb0095) 2009; 58
Bejjani, Saleki, Ballif (bb0065) 2005; 134
Mefford, Sharp, Baker (CR3) 2008; 359
Girirajan, Campbell, Eichler (CR2) 2011; 45
Lee, Lin, Lin, Shih, Lin, Su (CR19) 2012; 119
Girirajan, Rosenfeld, Coe (CR8) 2012; 367
Baird, Anderson, Newcombe, Lowry (CR15) 1988; 42
Ballif, Theisen, McDonald-McGinn (CR10) 2008; 74
Hubert, Van der Veeken (CR13) 2008; 22
Duker, Ballif, Bawle (CR11) 2010; 18
Ballif, Theisen, Coppinger (CR9) 2008; 1
Bejjani, Saleki, Ballif (CR12) 2005; 134
Girirajan, Eichler (CR1) 2010; 19
Shaffer, Dabell, Fisher (CR20) 2012; 32
Vassos, Collier, Holden (CR14) 2010; 19
Cooper, Coe, Girirajan (CR4) 2011; 43
Kaminsky, Kaul, Paschall (CR5) 2011; 13
Miller, Adam, Aradhya (CR6) 2010; 86
(CR18) 2009; 58
Walsh, Bracken (CR17) 2011; 13
van Bon, Mefford, Menten (CR16) 2009; 46
Shen, Dies, Holm (CR7) 2010; 125
Girirajan (10.1038/gim.2012.164_bb0010)
van Bon (10.1038/gim.2012.164_bb0085)
Walsh (10.1038/gim.2012.164_bb0090)
Kaminsky (10.1038/gim.2012.164_bb0030)
Baird (10.1038/gim.2012.164_bb0080)
Centers for Disease Control and Prevention (10.1038/gim.2012.164_bb0095) 2009; 58
Duker (10.1038/gim.2012.164_bb0060)
Vassos (10.1038/gim.2012.164_bb0075)
Cooper (10.1038/gim.2012.164_bb0025)
Ballif (10.1038/gim.2012.164_bb0055)
Shaffer (10.1038/gim.2012.164_bb0105)
Miller (10.1038/gim.2012.164_bb0035)
Shen (10.1038/gim.2012.164_bb0040)
Ballif (10.1038/gim.2012.164_bb0050)
Lee (10.1038/gim.2012.164_bb0100)
Bejjani (10.1038/gim.2012.164_bb0065)
Mefford (10.1038/gim.2012.164_bb0020)
Girirajan (10.1038/gim.2012.164_bb0045)
Hubert (10.1038/gim.2012.164_bb0070)
Girirajan (10.1038/gim.2012.164_bb0015)
23552451 - Genet Med. 2013 Apr;15(4):316-7. doi: 10.1038/gim.2013.16.
23552452 - Genet Med. 2013 Apr;15(4):317-8. doi: 10.1038/gim.2013.20.
References_xml – volume: 42
  start-page: 677
  year: 1988
  end-page: 693
  ident: bb0080
  article-title: Genetic disorders in children and young adults: a population study
  publication-title: Am J Hum Genet
– volume: 45
  start-page: 203
  year: 2011
  end-page: 226
  ident: bb0015
  article-title: Human copy number variation and complex genetic disease
  publication-title: Annu Rev Genet
– volume: 58
  start-page: 1
  year: 2009
  end-page: 20
  ident: bb0095
  article-title: Prevalence of autism spectrum disorders—Autism and Developmental Disabilities Monitoring Network, United States, 2006. Surveillance Summaries
  publication-title: Morb Mortal Wkly Rep
– volume: 86
  start-page: 749
  year: 2010
  end-page: 764
  ident: bb0035
  article-title: Consensus statement: chromosomal microarray is a first-tier clinical diagnostic test for individuals with developmental disabilities or congenital anomalies
  publication-title: Am J Hum Genet
– volume: 359
  start-page: 1685
  year: 2008
  end-page: 1699
  ident: bb0020
  article-title: Recurrent rearrangements of chromosome 1q21.1 and variable pediatric phenotypes
  publication-title: N Engl J Med
– volume: 43
  start-page: 838
  year: 2011
  end-page: 846
  ident: bb0025
  article-title: A copy number variation morbidity map of developmental delay [forthcoming corrigendum in Nat Genet]
  publication-title: Nat Genet
– volume: 74
  start-page: 469
  year: 2008
  end-page: 475
  ident: bb0055
  article-title: Identification of a previously unrecognized microdeletion syndrome of 16q11.2q12.2
  publication-title: Clin Genet
– volume: 1
  start-page: 8
  year: 2008
  ident: bb0050
  article-title: Expanding the clinical phenotype of the 3q29 microdeletion syndrome and characterization of the reciprocal microduplication
  publication-title: Mol Cytogenet
– volume: 19
  start-page: 3477
  year: 2010
  end-page: 3481
  ident: bb0075
  article-title: Penetrance for copy number variants associated with schizophrenia
  publication-title: Hum Mol Genet
– volume: 46
  start-page: 511
  year: 2009
  end-page: 523
  ident: bb0085
  article-title: Further delineation of the 15q13 microdeletion and duplication syndromes: a clinical spectrum varying from non-pathogenic to a severe outcome
  publication-title: J Med Genet
– volume: 32
  start-page: 976
  year: 2012
  end-page: 985
  ident: bb0105
  article-title: Experience with microarray-based comparative genomic hybridization for prenatal diagnosis in over 5000 pregnancies
  publication-title: Prenat Diagn
– volume: 119
  start-page: 614
  year: 2012
  end-page: 625
  ident: bb0100
  article-title: Clinical utility of array comparative genomic hybridisation for prenatal diagnosis: a cohort study of 3171 pregnancies
  publication-title: BJOG
– volume: 18
  start-page: 1196
  year: 2010
  end-page: 1201
  ident: bb0060
  article-title: Paternally inherited microdeletion at 15q11.2 confirms a significant role for the SNORD116 C/D box snoRNA cluster in Prader-Willi syndrome
  publication-title: Eur J Hum Genet
– volume: 367
  start-page: 1321
  year: 2012
  end-page: 1331
  ident: bb0045
  article-title: Phenotypic heterogeneity of genomic disorders and rare copy-number variants
  publication-title: N Engl J Med
– volume: 13
  start-page: 777
  year: 2011
  end-page: 784
  ident: bb0030
  article-title: An evidence-based approach to establish the functional and clinical significance of copy number variants in intellectual and developmental disabilities
  publication-title: Genet Med
– volume: 134
  start-page: 259
  year: 2005
  end-page: 267
  ident: bb0065
  article-title: Use of targeted array-based CGH for the clinical diagnosis of chromosomal imbalance: is less more
  publication-title: Am J Med Genet
– volume: 13
  start-page: 377
  year: 2011
  end-page: 384
  ident: bb0090
  article-title: Copy number variation in the dosage-sensitive 16p11.2 interval accounts for only a small proportion of autism incidence: a systematic review and meta-analysis
  publication-title: Genet Med
– volume: 125
  start-page: e727
  year: 2010
  end-page: e735
  ident: bb0040
  article-title: Clinical genetic testing for patients with autism spectrum disorders
  publication-title: Pediatrics
– volume: 19
  start-page: R176
  year: 2010
  end-page: R187
  ident: bb0010
  article-title: Phenotypic variability and genetic susceptibility to genomic disorders
  publication-title: Hum Mol Genet
– volume: 22
  start-page: 235
  year: 2008
  end-page: 246
  ident: bb0070
  article-title: Outlier detection for skewed data
  publication-title: J Chemometr
– volume: 359
  start-page: 1685
  year: 2008
  end-page: 1699
  ident: CR3
  article-title: Recurrent rearrangements of chromosome 1q21.1 and variable pediatric phenotypes
  publication-title: N Engl J Med
  doi: 10.1056/NEJMoa0805384
– volume: 19
  start-page: 3477
  year: 2010
  end-page: 3481
  ident: CR14
  article-title: Penetrance for copy number variants associated with schizophrenia
  publication-title: Hum Mol Genet
  doi: 10.1093/hmg/ddq259
– volume: 86
  start-page: 749
  year: 2010
  end-page: 764
  ident: CR6
  article-title: Consensus statement: chromosomal microarray is a first-tier clinical diagnostic test for individuals with developmental disabilities or congenital anomalies
  publication-title: Am J Hum Genet
  doi: 10.1016/j.ajhg.2010.04.006
– volume: 125
  start-page: e727
  year: 2010
  end-page: e735
  ident: CR7
  article-title: Clinical genetic testing for patients with autism spectrum disorders
  publication-title: Pediatrics
  doi: 10.1542/peds.2009-1684
– volume: 45
  start-page: 203
  year: 2011
  end-page: 226
  ident: CR2
  article-title: Human copy number variation and complex genetic disease
  publication-title: Annu Rev Genet
  doi: 10.1146/annurev-genet-102209-163544
– volume: 46
  start-page: 511
  year: 2009
  end-page: 523
  ident: CR16
  article-title: Further delineation of the 15q13 microdeletion and duplication syndromes: a clinical spectrum varying from non-pathogenic to a severe outcome
  publication-title: J Med Genet
  doi: 10.1136/jmg.2008.063412
– volume: 13
  start-page: 777
  year: 2011
  end-page: 784
  ident: CR5
  article-title: An evidence-based approach to establish the functional and clinical significance of copy number variants in intellectual and developmental disabilities
  publication-title: Genet Med
  doi: 10.1097/GIM.0b013e31822c79f9
– volume: 13
  start-page: 377
  year: 2011
  end-page: 384
  ident: CR17
  article-title: Copy number variation in the dosage-sensitive 16p11.2 interval accounts for only a small proportion of autism incidence: a systematic review and meta-analysis
  publication-title: Genet Med
  doi: 10.1097/GIM.0b013e3182076c0c
– volume: 22
  start-page: 235
  year: 2008
  end-page: 246
  ident: CR13
  article-title: Outlier detection for skewed data
  publication-title: J Chemometr
  doi: 10.1002/cem.1123
– volume: 32
  start-page: 976
  year: 2012
  end-page: 985
  ident: CR20
  article-title: Experience with microarray-based comparative genomic hybridization for prenatal diagnosis in over 5000 pregnancies
  publication-title: Prenat Diagn
  doi: 10.1002/pd.3945
– volume: 367
  start-page: 1321
  year: 2012
  end-page: 1331
  ident: CR8
  article-title: Phenotypic heterogeneity of genomic disorders and rare copy-number variants
  publication-title: N Engl J Med
  doi: 10.1056/NEJMoa1200395
– volume: 18
  start-page: 1196
  year: 2010
  end-page: 1201
  ident: CR11
  article-title: Paternally inherited microdeletion at 15q11.2 confirms a significant role for the SNORD116 C/D box snoRNA cluster in Prader-Willi syndrome
  publication-title: Eur J Hum Genet
  doi: 10.1038/ejhg.2010.102
– volume: 119
  start-page: 614
  year: 2012
  end-page: 625
  ident: CR19
  article-title: Clinical utility of array comparative genomic hybridisation for prenatal diagnosis: a cohort study of 3171 pregnancies
  publication-title: BJOG
  doi: 10.1111/j.1471-0528.2012.03279.x
– volume: 43
  start-page: 838
  year: 2011
  end-page: 846
  ident: CR4
  article-title: A copy number variation morbidity map of developmental delay [forthcoming corrigendum in Nat Genet]
  publication-title: Nat Genet
  doi: 10.1038/ng.909
– volume: 74
  start-page: 469
  year: 2008
  end-page: 475
  ident: CR10
  article-title: Identification of a previously unrecognized microdeletion syndrome of 16q11.2q12.2
  publication-title: Clin Genet
  doi: 10.1111/j.1399-0004.2008.01094.x
– volume: 42
  start-page: 677
  year: 1988
  end-page: 693
  ident: CR15
  article-title: Genetic disorders in children and young adults: a population study
  publication-title: Am J Hum Genet
– volume: 58
  start-page: 1
  year: 2009
  end-page: 20
  ident: CR18
  article-title: Prevalence of autism spectrum disorders—Autism and Developmental Disabilities Monitoring Network, United States, 2006. Surveillance Summaries
  publication-title: Morb Mortal Wkly Rep
– volume: 19
  start-page: R176
  year: 2010
  end-page: R187
  ident: CR1
  article-title: Phenotypic variability and genetic susceptibility to genomic disorders
  publication-title: Hum Mol Genet
  doi: 10.1093/hmg/ddq366
– volume: 134
  start-page: 259
  year: 2005
  end-page: 267
  ident: CR12
  article-title: Use of targeted array-based CGH for the clinical diagnosis of chromosomal imbalance: is less more
  publication-title: Am J Med Genet
  doi: 10.1002/ajmg.a.30621
– volume: 1
  start-page: 8
  year: 2008
  ident: CR9
  article-title: Expanding the clinical phenotype of the 3q29 microdeletion syndrome and characterization of the reciprocal microduplication
  publication-title: Mol Cytogenet
  doi: 10.1186/1755-8166-1-8
– ident: 10.1038/gim.2012.164_bb0040
– ident: 10.1038/gim.2012.164_bb0045
– ident: 10.1038/gim.2012.164_bb0055
– ident: 10.1038/gim.2012.164_bb0030
– ident: 10.1038/gim.2012.164_bb0050
– ident: 10.1038/gim.2012.164_bb0070
– volume: 58
  start-page: 1
  year: 2009
  ident: 10.1038/gim.2012.164_bb0095
  article-title: Prevalence of autism spectrum disorders—Autism and Developmental Disabilities Monitoring Network, United States, 2006. Surveillance Summaries
  publication-title: Morb Mortal Wkly Rep
– ident: 10.1038/gim.2012.164_bb0090
– ident: 10.1038/gim.2012.164_bb0065
– ident: 10.1038/gim.2012.164_bb0020
– ident: 10.1038/gim.2012.164_bb0010
– ident: 10.1038/gim.2012.164_bb0085
– ident: 10.1038/gim.2012.164_bb0105
– ident: 10.1038/gim.2012.164_bb0035
– ident: 10.1038/gim.2012.164_bb0025
– ident: 10.1038/gim.2012.164_bb0060
– ident: 10.1038/gim.2012.164_bb0075
– ident: 10.1038/gim.2012.164_bb0015
– ident: 10.1038/gim.2012.164_bb0100
– ident: 10.1038/gim.2012.164_bb0080
– reference: 23552452 - Genet Med. 2013 Apr;15(4):317-8. doi: 10.1038/gim.2013.20.
– reference: 23552451 - Genet Med. 2013 Apr;15(4):316-7. doi: 10.1038/gim.2013.16.
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Snippet Although an increasing number of copy-number variations are being identified as susceptibility loci for a variety of pediatric diseases, the penetrance of...
Purpose: Although an increasing number of copy-number variations are being identified as susceptibility loci for a variety of pediatric diseases, the...
Purpose:Although an increasing number of copy-number variations are being identified as susceptibility loci for a variety of pediatric diseases, the penetrance...
Purpose: Although an increasing number of copy-number variations are being identified as susceptibility loci for a variety of pediatric diseases, the...
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SubjectTerms 631/208/726/649/2157
631/208/727/2000
692/699
692/700/1720
Algorithms
Bayes Theorem
Biomedical and Life Sciences
Biomedicine
Brief Report
Case-Control Studies
copy-number variation
DNA Copy Number Variations
Genetic counseling
Genetic Loci
Genetic Predisposition to Disease
genomic disorder
Genotype
Human Genetics
Humans
Laboratory Medicine
microarray
Models, Genetic
Penetrance
prenatal diagnosis
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Title Estimates of penetrance for recurrent pathogenic copy-number variations
URI https://dx.doi.org/10.1038/gim.2012.164
https://link.springer.com/article/10.1038/gim.2012.164
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