以尿崩症为首发表现的朗格汉斯细胞组织细胞增生症一例报告及文献复习
郎格汉斯细胞组织细胞增生症(Langerhans cell histiocytosis,LCH)是以单核-巨噬细胞系统的郎格汉斯细胞(抗原提呈细胞)在一个器官或多个器官增殖为特点的疾病,临床少见。LCH多发生于儿童,成人罕见。LCH临床表现复杂,常与受累部位或器官的范围、多少有关,早期诊断困难。近日,我们收治1例以尿崩症为首发表现的LCH患者,现报道如下并进行文献复习。...
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Published in | 中华血液学杂志 Vol. 37; no. 10; pp. 919 - 920 |
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Main Author | |
Format | Journal Article |
Language | Chinese |
Published |
山西医科大学,太原,030001%山西大医院
2016
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Subjects | |
Online Access | Get full text |
ISSN | 0253-2727 |
DOI | 10.3760/cma.j.issn.0253-2727.2016.10.022 |
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Abstract | 郎格汉斯细胞组织细胞增生症(Langerhans cell histiocytosis,LCH)是以单核-巨噬细胞系统的郎格汉斯细胞(抗原提呈细胞)在一个器官或多个器官增殖为特点的疾病,临床少见。LCH多发生于儿童,成人罕见。LCH临床表现复杂,常与受累部位或器官的范围、多少有关,早期诊断困难。近日,我们收治1例以尿崩症为首发表现的LCH患者,现报道如下并进行文献复习。 |
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AbstractList | 郎格汉斯细胞组织细胞增生症(Langerhans cell histiocytosis,LCH)是以单核-巨噬细胞系统的郎格汉斯细胞(抗原提呈细胞)在一个器官或多个器官增殖为特点的疾病,临床少见。LCH多发生于儿童,成人罕见。LCH临床表现复杂,常与受累部位或器官的范围、多少有关,早期诊断困难。近日,我们收治1例以尿崩症为首发表现的LCH患者,现报道如下并进行文献复习。 @@ |
Author | 王燎 侯淑玲 王刚刚 张巧花 |
AuthorAffiliation | 山西医科大学,太原030001 山西大医院 |
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Notes | Wang Liao, Hou Shuling, Wang Ganggang, Zhang Qiaohua ( Department of Oncology III (lymphoma), Shanxi Academy of Medical Sciences Shanxi Dayi Hospital Taiyuan 030032, China) 12-1090/R |
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SubjectTerms | histiocytosis 单核-巨噬细胞系统 尿崩症 抗原提呈细胞 文献复习 朗格汉斯细胞组织细胞增生症 郎格汉斯细胞组织细胞增生症 首发表现 |
Title | 以尿崩症为首发表现的朗格汉斯细胞组织细胞增生症一例报告及文献复习 |
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