Nearly fatal ventricular arrhythmia following pacemaker implantation in a young female with complete heart block
This case concerns a 24‐year‐old female who developed malignant ventricular tachyarrhythmia a few weeks after pacemaker implantation for complete heart block. Apparently, right ventricular pacing caused significant repolarization abnormalities in both native and paced rhythms with marked QT prolonga...
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| Published in | Journal of arrhythmia Vol. 35; no. 5; pp. 766 - 769 |
|---|---|
| Main Authors | , , , , , , , , |
| Format | Journal Article |
| Language | English |
| Published |
Hoboken
John Wiley & Sons, Inc
01.10.2019
John Wiley and Sons Inc Wiley |
| Subjects | |
| Online Access | Get full text |
| ISSN | 1880-4276 1883-2148 1883-2148 |
| DOI | 10.1002/joa3.12220 |
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| Abstract | This case concerns a 24‐year‐old female who developed malignant ventricular tachyarrhythmia a few weeks after pacemaker implantation for complete heart block. Apparently, right ventricular pacing caused significant repolarization abnormalities in both native and paced rhythms with marked QT prolongation and substantial electrical instability. This case highlights other intriguing phenomena in the puzzle of cardiac repolarization and how pacing therapy may alter this complex process providing arrhythmic substrate in vulnerable subjects. Though such arrhythmic events are clinically rare, vulnerable patients or with suspected myocardial disease that may cause QT prolongation should be carefully followed in the course of pacing therapy. |
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| AbstractList | This case concerns a 24-year-old female who developed malignant ventricular tachyarrhythmia a few weeks after pacemaker implantation for complete heart block. Apparently, right ventricular pacing caused significant repolarization abnormalities in both native and paced rhythms with marked QT prolongation and substantial electrical instability. This case highlights other intriguing phenomena in the puzzle of cardiac repolarization and how pacing therapy may alter this complex process providing arrhythmic substrate in vulnerable subjects. Though such arrhythmic events are clinically rare, vulnerable patients or with suspected myocardial disease that may cause QT prolongation should be carefully followed in the course of pacing therapy.This case concerns a 24-year-old female who developed malignant ventricular tachyarrhythmia a few weeks after pacemaker implantation for complete heart block. Apparently, right ventricular pacing caused significant repolarization abnormalities in both native and paced rhythms with marked QT prolongation and substantial electrical instability. This case highlights other intriguing phenomena in the puzzle of cardiac repolarization and how pacing therapy may alter this complex process providing arrhythmic substrate in vulnerable subjects. Though such arrhythmic events are clinically rare, vulnerable patients or with suspected myocardial disease that may cause QT prolongation should be carefully followed in the course of pacing therapy. Abstract This case concerns a 24‐year‐old female who developed malignant ventricular tachyarrhythmia a few weeks after pacemaker implantation for complete heart block. Apparently, right ventricular pacing caused significant repolarization abnormalities in both native and paced rhythms with marked QT prolongation and substantial electrical instability. This case highlights other intriguing phenomena in the puzzle of cardiac repolarization and how pacing therapy may alter this complex process providing arrhythmic substrate in vulnerable subjects. Though such arrhythmic events are clinically rare, vulnerable patients or with suspected myocardial disease that may cause QT prolongation should be carefully followed in the course of pacing therapy. This case concerns a 24-year-old female who developed malignant ventricular tachyarrhythmia a few weeks after pacemaker implantation for complete heart block. Apparently, right ventricular pacing caused significant repolarization abnormalities in both native and paced rhythms with marked QT prolongation and substantial electrical instability. This case highlights other intriguing phenomena in the puzzle of cardiac repolarization and how pacing therapy may alter this complex process providing arrhythmic substrate in vulnerable subjects. Though such arrhythmic events are clinically rare, vulnerable patients or with suspected myocardial disease that may cause QT prolongation should be carefully followed in the course of pacing therapy. |
| Audience | Academic |
| Author | De Lucia, Carmine Foresti, Sara De Ambroggi, Guido Lupo, Pierpaolo Ali, Hussam Mantovani, Riccardo Cappato, Riccardo Passarelli, Ilaria De Ambroggi, Luigi |
| AuthorAffiliation | 1 Arrhythmia & EP Research Center IRCCS Humanitas Research & University Hospital Rozzano (Milan) Italy 2 University of Milan Milan Italy |
| AuthorAffiliation_xml | – name: 2 University of Milan Milan Italy – name: 1 Arrhythmia & EP Research Center IRCCS Humanitas Research & University Hospital Rozzano (Milan) Italy |
| Author_xml | – sequence: 1 givenname: Hussam orcidid: 0000-0002-3469-1028 surname: Ali fullname: Ali, Hussam email: hussamali.ep@gmail.com organization: IRCCS Humanitas Research & University Hospital – sequence: 2 givenname: Pierpaolo surname: Lupo fullname: Lupo, Pierpaolo organization: IRCCS Humanitas Research & University Hospital – sequence: 3 givenname: Sara surname: Foresti fullname: Foresti, Sara organization: IRCCS Humanitas Research & University Hospital – sequence: 4 givenname: Guido surname: De Ambroggi fullname: De Ambroggi, Guido organization: IRCCS Humanitas Research & University Hospital – sequence: 5 givenname: Riccardo surname: Mantovani fullname: Mantovani, Riccardo organization: IRCCS Humanitas Research & University Hospital – sequence: 6 givenname: Carmine surname: De Lucia fullname: De Lucia, Carmine organization: IRCCS Humanitas Research & University Hospital – sequence: 7 givenname: Ilaria surname: Passarelli fullname: Passarelli, Ilaria organization: IRCCS Humanitas Research & University Hospital – sequence: 8 givenname: Luigi surname: De Ambroggi fullname: De Ambroggi, Luigi organization: University of Milan – sequence: 9 givenname: Riccardo surname: Cappato fullname: Cappato, Riccardo organization: IRCCS Humanitas Research & University Hospital |
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| Cites_doi | 10.1016/j.hrthm.2014.08.026 10.1016/0002-9149(82)90169-2 10.1161/01.CIR.100.24.2431 10.1111/jce.13203 10.1111/jce.12179 |
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| Copyright | 2019 The Authors. published by John Wiley & Sons Australia, Ltd on behalf of the Japanese Heart Rhythm Society. COPYRIGHT 2019 John Wiley & Sons, Inc. 2019 The Authors. Journal of Arrhythmia published by John Wiley & Sons Australia, Ltd on behalf of the Japanese Heart Rhythm Society. |
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| References | 1982; 50 2017; 28 2013; 24 2014; 11 1999; 100 e_1_2_6_3_1 e_1_2_6_2_1 e_1_2_6_5_1 e_1_2_6_4_1 e_1_2_6_6_1 |
| References_xml | – volume: 100 start-page: 2431 issue: 24 year: 1999 end-page: 6 article-title: Long‐term follow‐up of patients with long‐QT syndrome treated with beta‐blockers and continuous pacing publication-title: Circulation – volume: 24 start-page: 1304 issue: 11 year: 2013 end-page: 5 article-title: Proarrhythmic effect of pacing mode reprogramation in a patient with a congenital long‐QT syndrome publication-title: J Cardiovasc Electrophysiol – volume: 50 start-page: 213 issue: 2 year: 1982 end-page: 22 article-title: Electrotonic modulation of the T wave and cardiac memory publication-title: Am J Cardiol – volume: 11 start-page: 2273 issue: 12 year: 2014 end-page: 7 article-title: New formula for evaluation of the QT interval in patients with left bundle branch block publication-title: Heart Rhythm – volume: 28 start-page: 684 issue: 6 year: 2017 end-page: 9 article-title: A new formula for estimating the true QT interval in left bundle branch block publication-title: J Cardiovasc Electrophysiol – ident: e_1_2_6_3_1 doi: 10.1016/j.hrthm.2014.08.026 – ident: e_1_2_6_2_1 doi: 10.1016/0002-9149(82)90169-2 – ident: e_1_2_6_5_1 doi: 10.1161/01.CIR.100.24.2431 – ident: e_1_2_6_4_1 doi: 10.1111/jce.13203 – ident: e_1_2_6_6_1 doi: 10.1111/jce.12179 |
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| Snippet | This case concerns a 24‐year‐old female who developed malignant ventricular tachyarrhythmia a few weeks after pacemaker implantation for complete heart block.... This case concerns a 24-year-old female who developed malignant ventricular tachyarrhythmia a few weeks after pacemaker implantation for complete heart block.... Abstract This case concerns a 24‐year‐old female who developed malignant ventricular tachyarrhythmia a few weeks after pacemaker implantation for complete... |
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| SubjectTerms | Cardiac patients Case Report Case Reports complete heart block Disease susceptibility Heart Heart block long QT pacemaker Tachycardia ventricular repolarization ventricular tachyarrhythmia |
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| Title | Nearly fatal ventricular arrhythmia following pacemaker implantation in a young female with complete heart block |
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