Sustained Expression of Negative Regulators of Myelination Protects Schwann Cells from Dysmyelination in a Charcot–Marie–Tooth 1B Mouse Model - Florio, Francesca; Ferri, Cinzia; Scapin, Cristina; Feltri, M. Laura; Wrabetz, Lawrence; D'Antonio, Maurizio (The Journal of neuroscience, 2018)
Keywords: Ablation; Activation; Animals; Biocompatibility; Cell Differentiation; Charcot-Marie-Tooth disease; Charcot-Marie-Tooth Disease - genetics; Charcot-Marie-Tooth Disease - pathology; Demyelinating Diseases - genetics; Demyelinating Diseases - pathology; Demyelination; Differentiation (biology); Down-regulation; Endoplasmic Reticulum Stress - genetics; Female; Inhibitor of Differentiation Protein 2 - genetics; Male; Mice; Mice, Knockout; Mutants; Myelin P0 protein; Myelin Sheath - pathology; Myelination; Neuropathy; Phenotypes; Protein folding; Proteins; Regulators; Repair; Rodents; Schwann cells; Schwann Cells - pathology; SOXB1 Transcription Factors - genetics; Transcription factors; Unfolded Protein Response; myelin; Sox2; Charcot–Marie–Tooth; Schwann cell; Id2; UPR