The spectrum of α- and β-thalassemia mutations of the Li people in Hainan Province of China

This study examines the frequency and spectrum of α- and β-thalassemia (thal) mutations of the Li people in Hainan Province of China. We have analyzed by genotyping a sample of 8600 subjects of the Li people and found that 53.45% subjects have only α-thal mutations with high frequencies of −α4.2 and...

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Published inBlood cells, molecules, & diseases Vol. 53; no. 1-2; pp. 16 - 20
Main Authors Yao, Hongxia, Chen, Xinping, Lin, Lie, Wu, Congming, Fu, Xiangjun, Wang, Hua, Yao, Zhiming, Chen, Wenting, Huang, Li, Tang, Ruimei, Rao, Ruo, Wang, Suwen, Ding, Yipeng
Format Journal Article
LanguageEnglish
Published United States Elsevier Inc 01.06.2014
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Online AccessGet full text
ISSN1079-9796
1096-0961
1096-0961
DOI10.1016/j.bcmd.2014.01.003

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Abstract This study examines the frequency and spectrum of α- and β-thalassemia (thal) mutations of the Li people in Hainan Province of China. We have analyzed by genotyping a sample of 8600 subjects of the Li people and found that 53.45% subjects have only α-thal mutations with high frequencies of −α4.2 and −α3.7, but fewer −−SEA mutation; 3.83% have β-thal mutations all identified to be 41/42 (−TCTT); whereas 7.99% carry both α-thal and β-thal mutations. We also examined 9800 subjects of the Han people, and the result showed 12.16% subjects have only α-thal mutations with −−SEA and −α3.7 the most frequent mutation types, 6.11% have only β-thal mutations of 7 types, whereas 4.85% carry both α-thal and β-thal mutations. Our study demonstrated that the Li people in Hainan province have a high incidence of −α4.2 and −α3.7 thalassemia, low frequencies of α-thal −SEA, and a novel β mutation, 41/42 (−TCTT). We provide the complete spectrum of α-thal and β-thal mutations and a strategy for accurate molecular diagnostic testing in the Li people in Hainan Province of Southern China.
AbstractList This study examines the frequency and spectrum of α- and β-thalassemia (thal) mutations of the Li people in Hainan Province of China. We have analyzed by genotyping a sample of 8600 subjects of the Li people and found that 53.45% subjects have only α-thal mutations with high frequencies of -α(4.2) and -α(3.7), but fewer --(SEA) mutation; 3.83% have β-thal mutations all identified to be 41/42 (-TCTT); whereas 7.99% carry both α-thal and β-thal mutations. We also examined 9800 subjects of the Han people, and the result showed 12.16% subjects have only α-thal mutations with --(SEA) and -α(3.7) the most frequent mutation types, 6.11% have only β-thal mutations of 7 types, whereas 4.85% carry both α-thal and β-thal mutations. Our study demonstrated that the Li people in Hainan province have a high incidence of -α(4.2) and -α(3.7) thalassemia, low frequencies of α-thal -(SEA), and a novel β mutation, 41/42 (-TCTT). We provide the complete spectrum of α-thal and β-thal mutations and a strategy for accurate molecular diagnostic testing in the Li people in Hainan Province of Southern China.
This study examines the frequency and spectrum of α- and β-thalassemia (thal) mutations of the Li people in Hainan Province of China. We have analyzed by genotyping a sample of 8600 subjects of the Li people and found that 53.45% subjects have only α-thal mutations with high frequencies of -α(4.2) and -α(3.7), but fewer --(SEA) mutation; 3.83% have β-thal mutations all identified to be 41/42 (-TCTT); whereas 7.99% carry both α-thal and β-thal mutations. We also examined 9800 subjects of the Han people, and the result showed 12.16% subjects have only α-thal mutations with --(SEA) and -α(3.7) the most frequent mutation types, 6.11% have only β-thal mutations of 7 types, whereas 4.85% carry both α-thal and β-thal mutations. Our study demonstrated that the Li people in Hainan province have a high incidence of -α(4.2) and -α(3.7) thalassemia, low frequencies of α-thal -(SEA), and a novel β mutation, 41/42 (-TCTT). We provide the complete spectrum of α-thal and β-thal mutations and a strategy for accurate molecular diagnostic testing in the Li people in Hainan Province of Southern China.This study examines the frequency and spectrum of α- and β-thalassemia (thal) mutations of the Li people in Hainan Province of China. We have analyzed by genotyping a sample of 8600 subjects of the Li people and found that 53.45% subjects have only α-thal mutations with high frequencies of -α(4.2) and -α(3.7), but fewer --(SEA) mutation; 3.83% have β-thal mutations all identified to be 41/42 (-TCTT); whereas 7.99% carry both α-thal and β-thal mutations. We also examined 9800 subjects of the Han people, and the result showed 12.16% subjects have only α-thal mutations with --(SEA) and -α(3.7) the most frequent mutation types, 6.11% have only β-thal mutations of 7 types, whereas 4.85% carry both α-thal and β-thal mutations. Our study demonstrated that the Li people in Hainan province have a high incidence of -α(4.2) and -α(3.7) thalassemia, low frequencies of α-thal -(SEA), and a novel β mutation, 41/42 (-TCTT). We provide the complete spectrum of α-thal and β-thal mutations and a strategy for accurate molecular diagnostic testing in the Li people in Hainan Province of Southern China.
This study examines the frequency and spectrum of α- and β-thalassemia (thal) mutations of the Li people in Hainan Province of China. We have analyzed by genotyping a sample of 8600 subjects of the Li people and found that 53.45% subjects have only α-thal mutations with high frequencies of −α4.2 and −α3.7, but fewer −−SEA mutation; 3.83% have β-thal mutations all identified to be 41/42 (−TCTT); whereas 7.99% carry both α-thal and β-thal mutations. We also examined 9800 subjects of the Han people, and the result showed 12.16% subjects have only α-thal mutations with −−SEA and −α3.7 the most frequent mutation types, 6.11% have only β-thal mutations of 7 types, whereas 4.85% carry both α-thal and β-thal mutations. Our study demonstrated that the Li people in Hainan province have a high incidence of −α4.2 and −α3.7 thalassemia, low frequencies of α-thal −SEA, and a novel β mutation, 41/42 (−TCTT). We provide the complete spectrum of α-thal and β-thal mutations and a strategy for accurate molecular diagnostic testing in the Li people in Hainan Province of Southern China.
Author Yao, Hongxia
Wu, Congming
Huang, Li
Wang, Suwen
Chen, Wenting
Chen, Xinping
Tang, Ruimei
Rao, Ruo
Lin, Lie
Yao, Zhiming
Ding, Yipeng
Fu, Xiangjun
Wang, Hua
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  givenname: Yipeng
  surname: Ding
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Issue 1-2
Keywords Hainan Province
Thalassemia
Han people
Population genetics
Li people
Genetic diagnosis
Language English
License Copyright © 2014 Elsevier Inc. All rights reserved.
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Snippet This study examines the frequency and spectrum of α- and β-thalassemia (thal) mutations of the Li people in Hainan Province of China. We have analyzed by...
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StartPage 16
SubjectTerms Adolescent
Adult
Aged
Aged, 80 and over
Alleles
alpha-Globins - genetics
alpha-Thalassemia - epidemiology
alpha-Thalassemia - genetics
beta-Globins - genetics
beta-Thalassemia - epidemiology
beta-Thalassemia - genetics
Child
Child, Preschool
China - epidemiology
Ethnic Groups - genetics
Gene Frequency
Genetic diagnosis
Genotype
Geography
Hainan Province
Han people
Humans
Incidence
Infant
Li people
Middle Aged
Mutation
Phenotype
Population genetics
Thalassemia
Young Adult
Title The spectrum of α- and β-thalassemia mutations of the Li people in Hainan Province of China
URI https://dx.doi.org/10.1016/j.bcmd.2014.01.003
https://www.ncbi.nlm.nih.gov/pubmed/24534675
https://www.proquest.com/docview/1526131385
Volume 53
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