腺泡状软组织肉瘤的临床及影像学表现

【目的】 总结腺泡状软组织肉瘤(ASPS)的临床病理、磁共振(MRI)及多层螺旋CT(MSCT)特点。 【方法】 收集经病理证实的27例ASPS的资料,分析其临床病理及影像学特点。 【结果】 (1)女性11例,男性16例,平均年龄28.7岁。临床表现为无痛性肿块19例;疼痛4例,伴肿瘤远端肢体功能障碍2例;鼻塞、耳鸣1例;体检发现肿物3例。肿瘤平均最大径7.1 cm,位于下肢12例、躯干12例、颌面部3例。(2)术后病理均示瘤细胞呈腺泡状排列,胞浆丰富,内含红染颗粒,核仁明显;糖元染色(PAS)阳性。(3) MRI检查20例:T1WI低信号2例,等信号4例,稍高信号14例;T2WI高信号;6例...

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Published inZhongshan da xue xue bao. Zhongshan daxue xuebao yixue kexue ban = Journal of Sun Yat-sen University. Yi xue ke xue ban Vol. 34
Format Journal Article
LanguageChinese
Published Editorial Office of Journal of Sun Yat-sen University 01.01.2013
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ISSN1672-3554

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Abstract 【目的】 总结腺泡状软组织肉瘤(ASPS)的临床病理、磁共振(MRI)及多层螺旋CT(MSCT)特点。 【方法】 收集经病理证实的27例ASPS的资料,分析其临床病理及影像学特点。 【结果】 (1)女性11例,男性16例,平均年龄28.7岁。临床表现为无痛性肿块19例;疼痛4例,伴肿瘤远端肢体功能障碍2例;鼻塞、耳鸣1例;体检发现肿物3例。肿瘤平均最大径7.1 cm,位于下肢12例、躯干12例、颌面部3例。(2)术后病理均示瘤细胞呈腺泡状排列,胞浆丰富,内含红染颗粒,核仁明显;糖元染色(PAS)阳性。(3) MRI检查20例:T1WI低信号2例,等信号4例,稍高信号14例;T2WI高信号;6例信号均匀,14例含坏死区。MSCT检查9例:平扫低密度1例,等密度4例,略高及混杂密度各2例;增强扫描肿瘤均明显强化,坏死区无强化;4例瘤内、4例瘤周、19例瘤内和瘤周见大量迂曲血管。骨原发ASPS或ASPS骨转移影像特点与软组织来源者相似。 【结论】 ASPS为富血供恶性肿瘤,其临床、影像及病理表现具有一定特征性。
AbstractList 【目的】 总结腺泡状软组织肉瘤(ASPS)的临床病理、磁共振(MRI)及多层螺旋CT(MSCT)特点。 【方法】 收集经病理证实的27例ASPS的资料,分析其临床病理及影像学特点。 【结果】 (1)女性11例,男性16例,平均年龄28.7岁。临床表现为无痛性肿块19例;疼痛4例,伴肿瘤远端肢体功能障碍2例;鼻塞、耳鸣1例;体检发现肿物3例。肿瘤平均最大径7.1 cm,位于下肢12例、躯干12例、颌面部3例。(2)术后病理均示瘤细胞呈腺泡状排列,胞浆丰富,内含红染颗粒,核仁明显;糖元染色(PAS)阳性。(3) MRI检查20例:T1WI低信号2例,等信号4例,稍高信号14例;T2WI高信号;6例信号均匀,14例含坏死区。MSCT检查9例:平扫低密度1例,等密度4例,略高及混杂密度各2例;增强扫描肿瘤均明显强化,坏死区无强化;4例瘤内、4例瘤周、19例瘤内和瘤周见大量迂曲血管。骨原发ASPS或ASPS骨转移影像特点与软组织来源者相似。 【结论】 ASPS为富血供恶性肿瘤,其临床、影像及病理表现具有一定特征性。
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Snippet 【目的】 总结腺泡状软组织肉瘤(ASPS)的临床病理、磁共振(MRI)及多层螺旋CT(MSCT)特点。 【方法】 收集经病理证实的27例ASPS的资料,分析其临床病理及影像学特点。 【结果】...
SourceID doaj
SourceType Open Website
SubjectTerms 体层摄影术,X线计算机
磁共振成像
腺泡状软组织肉瘤
Title 腺泡状软组织肉瘤的临床及影像学表现
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