Systemic Fibroinflammatory Disorders

This book provides detailed information on the nosology, pathology, pathogenesis, clinical presentation, diagnosis and treatment of fibro-inflammatory disorders, rare diseases that often display systemic organ involvement. Among the conditions considered are IgG4-related disease, sclerosing cholangi...

Full description

Saved in:
Bibliographic Details
Corporate Author SpringerLink (Online service)
Other Authors Vaglio, Augusto (Editor)
Format Electronic eBook
LanguageEnglish
Published Cham : Springer International Publishing : Imprint: Springer, 2017.
SeriesRare Diseases of the Immune System,
Subjects
Online AccessFull text
ISBN9783319413495
ISSN2282-6505
DOI10.1007/978-3-319-41349-5
Physical DescriptionXII, 243 p. 33 illus., 22 illus. in color. online resource.

Cover

Table of Contents:
  • Preface
  • 1 Genetics of fibro-inflammatory disorders
  • 2 Basic mechanisms linking inflammation and fibrosis
  • 3 Histopathology of systemic fibro-inflammatory disorders
  • 4 IgG4-related disorders: clinical and therapeutic aspects
  • 5 IgG4-related disorders: pathophysiology
  • 6 IgG4-related nephropathy
  • 7 Autoimmune (IgG4-related) pancreatitis and sclerosing cholangitis
  • 8 Sclerosing forms of autoimmune thyroiditis: from Hashimoto's to Riedel's to IgG4-related forms
  • 9 Chronic periaortitis/retroperitoneal fibrosis: overview
  • 10 Diffuse periaortitis
  • 11 Treatment of chronic periaortitis/retroperitoneal fibrosis
  • 12 Mediastinal fibrosis
  • 13 Erdheim-Chester disease
  • 14 Nephrogenic systemic fibrosis
  • 15 Sclerosing mesenteritis
  • 16 Malignant diseases mimicking retroperitoneal fibrosing disorders
  • Subject Index.